The importance of adequate dental management to the patient with Cleidocranial Dysostosis: Case report
Cleidocranial Dysostosis (CCD) is characterized as a rare autosomal dominant genetic syndrome with no gender preference, characterized by a defect in the gene CBFA1 of chromosome 6p21, which modulate the formation of osteoblasts. Its clinical characteristics are clavicle aplasia or hypoplasia, changes in skeletal level with influence on the anatomical structure of the wearer and polydontia. There is no specific treatment, and the main conduct is to offer the best possible quality of life to the bearer, and this involves oral health.